Volume 22, Issue 2 (Pajouhan Scientific Journal, Spring 2024)                   Pajouhan Sci J 2024, 22(2): 119-127 | Back to browse issues page

Ethics code: IR.UMSHA.REC.1401.863


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Jamali Delfan R, Heshmati A, Zanganeh M, Sharifi A. Assessment of Growth Indices in Children and Adolescents with Phenylketonuria in Hamadan City, 2023. Pajouhan Sci J 2024; 22 (2) :119-127
URL: http://psj.umsha.ac.ir/article-1-1094-en.html
1- Student Research Committee, Faculty of Medicine, Hamadan University of Medical Sciences, Hamadan, Iran
2- Department of Nutrition and Food Hygiene, Nutrition Health Research Center, Faculty of Medicine, Hamadan University of Medical Sciences, Hamadan, Iran
3- Clinical Research Center, Besat Hospital, Hamadan University of Medical Sciences, Hamadan, Iran
4- Department of Nutrition and Food Hygiene, Nutrition Health Research Center, Faculty of Medicine, Hamadan University of Medical Sciences, Hamadan, Iran , a.sharifi1983@gmail.com
Abstract:   (1645 Views)
Background and Objectives: Dietary restrictions in phenylketonuria (PKU) can prevent children’s normal growth, and compensatory intake of carbohydrates and fats can cause excessive weight gain. This study aimed to investigate some growth indicators in PKU patients aged 6 months to 18 years in Hamadan City in 2023.
Materials and Methods: In this cross-sectional analytical study, the height, weight, and age of all patients ranging in age from 6 months to 18 years, who were registered at the PKU Center of Besat Hospital in Hamedan, were measured and recorded. Body mass index (BMI) was calculated using height and weight information. In addition, the corresponding z-scores were calculated using the online growth calculator software. Z-score values were classified into five levels using World Health Organization criteria.
Results: In this study, 80 PKU patients (including 44 girls and 36 boys) were examined. The average age, as well as the average Z-score of height, weight, and BMI for age, were not significantly different in boys and girls. Moreover, 7.5% of children were underweight, 1.3% were severely underweight, 10% were stunted, and 2.5% were severely stunted. Ten percent of children were severely wasted and 6.3% were wasted. On the other hand, 11.3% were overweight. None of these children were obese.
Conclusion: In addition to controlling the dietary intake of phenylalanine, it is necessary to continuously monitor the growth indicators of these children and also to control the intake of calories, macronutrients, and micronutrients accurately based on the child's needs.
Full-Text [PDF 1138 kb]   (323 Downloads)    
Type of Study: Research Article | Subject: Health Sciences
Received: 2024/05/14 | Accepted: 2024/05/29 | Published: 2024/07/31

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